Clinical Signs (other than ataxia) | ADCA type 1 |
---|---|
Slow Saccades | SCA1, SCA2, SCA3, and SCA7 |
Ophthalmoplegia | SCA1, SCA2 and SCA3 |
UMN signs | SCA1, SCA3, and SCA12 (sometimes SCA8) |
Extrapyramidal | SCA3, and SCA12 (Parkinsonism) SCA3 (Dystonia) SCA2, and occasionally SCA1, SCA3, and SCA19(Myoclonus) SCA12, SCA16, SCA19 |
Cortical | SCA13, SCA21 SCA17 (Dementia, psychosis, and epilepsy) |
Pontine Signs | SCA1, SCA2, and SCA3 |
Fasciculations | SCA3 |
Peripheral Neuropathy | SCA3, SCA4, SCA18 |