Case | Diet during initial hyper-ammonemic crisis | Pre-carbamylglutamate diet |
---|---|---|
1 Age at Dietary Record Calories (kcal/kg/day) Protein (g/kg/day) Arginine (mg/kg/day) Citrulline (mg/kg/day) | 3 days 68 1 250 0 | 39 days 117 1.6 0 200 |
2 Age at Dietary Record Calories (kcal/kg/day) Protein (g/kg/day) Arginine (mg/kg/day) Citrulline (mg/kg/day) | 6 days 120 0 0 0 | 24 days 130 1.0 250 0 |
3 Age at Dietary Record Calories (kcal/kg/day) Protein (g/kg/day) Arginine (mg/kg/day) Citrulline (mg/kg/day) | 38 years 46 1.4 0 0 | 39 years Not available 1.0 0 50 |
4 Age at Dietary Record Calories (kcal/kg/day) Protein (g/kg/day) Arginine (mg/kg/day) Citrulline (mg/kg/day) | 25 months 122 1.2 0 170 | 28 months 64 1.05–1.2 0 160 |
5 Age at Dietary Record Calories (kcal/kg/day) Protein (g/kg/day) Arginine (mg/kg/day) Citrulline (mg/kg/day) | 14 years 35 0 0 150 | 18 years 30 0.5 0 150 |
6 Age at Dietary Record Calories (kcal/kg/day) Protein (g/kg/day) Arginine (mg/kg/day) Citrulline (mg/kg/day) | 10 years 17 0 114 0 | 18 years 18.8 0.47 0 130 |
7 Age at Dietary Record Calories (kcal/kg/day) Protein (g/kg/day) Arginine (mg/kg/day) Citrulline (mg/kg/day) | 2 years 28 0.36 0 210 | 22 years 28 0.45 0 200 |