Type of OI | Mild OI type I | Moderate OI type IV | Severe OI type III | All | Ā |
---|---|---|---|---|---|
Sociodemographic characteristics | |||||
Enrollment numberā n (%) | 20 [31] | 31 [47] | 14 [21] | 65 (100) | Ā |
Female | 18 (90) | 19 (61) | 9 (64) | 46 (70) | Ā |
Ageā Average Range | 29 | 35 | 35 | - | Ā |
Educational levelā n (%) | |||||
Some college - high school or less | Ā | ||||
College graduateā postgraduate | Ā | ||||
Pertinent Medical Conditions | |||||
Genetic mutationā n (%) | |||||
Col1A1 - Col1A2 | 16 (80) āā2 [10] | 19 (61) āā7 [23] | 40 (62) āā12 [19] | Ā | |
Othersā unsure | 0 (0) āā2 [10] | Ā | |||
OI medicationsā n (%) | |||||
Bisphosphonateā+āother types of drugsā Yes | 10 [13] | 18 (58) | 9 (64) | 37 (57) | Ā |
Bisphosphonate | 8 (80) | 12 (67) | 4 [45] | 24 (65) | Ā |
Oralā IV | 3 (37.5)ā 5 (62.5) | 1 (8.3)-11 (91.7) | 1 [25]- 3 (75) | 5 (20.8)ā 19 (79.2) | Ā |
Denosumab (Prolia) | 0 (0) | 3 [17] | 1 [11] | 4 [11] | Ā |
Teriparatide (Forsteo) | 1 [10] | 0 (0) | 1 [11] | 2 [5] | Ā |
Other types of drugs | 1 [10] | 3 [17] | 3 [33] | 7 [19] | Ā |
Vit D intakeā Yes | 12 (60) | 26 (84) | 12 (86) | 50 (77) | Ā |
Calcium intakeā Yes | 12 (60) | 14 [45] | 10 (72) | 36 (55) | Ā |
Oral Conditions | |||||
Enrollment numberā n (%) | 9 [36] | 10 [44] | 5 [20] | 24 (100) | Ā |
DI (Yes)ā n (%) | 2 [22] | 5 [13] | 1 [20] | 8 [33] | Ā |
Molar classificationā n (%) | Ā | ||||
Cl | 6 (67) | 3 [30] | 0 (0) | 9 [38] | Ā |
Clll | 2 [22] | 4 [40] | 3 (60) | 9 [38] | Ā |
Cll and neglected* | 1 [11] | 3 [30] | 2 [40] | 6 [24] | Ā |
Anterior open biteā n (%) Yes | 0 (0) | 2 [20] | 3 (60) | 5 [21] | Ā |
Posterior open biteā n (%) Yes | 1 [11] | 0 (0) | 3 (60) | 4 [17] | Ā |
Anterior crossbiteā n (%) Yes | 0 (0) | 3 [30] | 3 (60) | 6 [25] | Ā |
Posterior crossbiteā n (%) Yes | 1 [11] | 3 [30] | 3 (60) | 7 [29] | Ā |