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Table 1 Characteristics of adults with OI and their oral condition

From: The impact of osteogenesis imperfecta severity on oral health-related quality of life in Spain: a cross-sectional study

Type of OI

Mild OI

type I

Moderate OI

type IV

Severe OI

type III

All

Ā 

Sociodemographic characteristics

Enrollment numberā€“ n (%)

20 [31]

31 [47]

14 [21]

65 (100)

Ā 

Female

18 (90)

19 (61)

9 (64)

46 (70)

Ā 

Ageā€“ Average Range

29

35

35

-

Ā 

Educational levelā€“ n (%)

Some college - high school or less

2 [10] āˆ’ā€‰6 [30]

8 [26] āˆ’ā€‰13 [41]

4 [29] āˆ’ā€‰7 [13]

14 [22] āˆ’ā€‰25 [39]

Ā 

College graduateā€“ postgraduate

8 [40] āˆ’ā€‰4 [20]

7 [23] āˆ’ā€‰3 [10]

20 [14] āˆ’ā€‰1 [7]

17 [27] āˆ’ā€‰8 [12]

Ā 

Pertinent Medical Conditions

Genetic mutationā€“ n (%)

Col1A1 - Col1A2

16 (80) āˆ’ā€‰2 [10]

19 (61) āˆ’ā€‰7 [23]

5 [36] āˆ’ā€‰4 [29]

40 (62) āˆ’ā€‰12 [19]

Ā 

Othersā€“ unsure

0 (0) āˆ’ā€‰2 [10]

1 [3] āˆ’ā€‰4 [13]

3 [21] āˆ’ā€‰2 [14]

4 [6] āˆ’ā€‰8 [13]

Ā 

OI medicationsā€“ n (%)

Bisphosphonateā€‰+ā€‰other types of drugsā€“ Yes

10 [13]

18 (58)

9 (64)

37 (57)

Ā 

Bisphosphonate

8 (80)

12 (67)

4 [45]

24 (65)

Ā 

Oralā€“ IV

3 (37.5)ā€“ 5 (62.5)

1 (8.3)-11 (91.7)

1 [25]- 3 (75)

5 (20.8)ā€“ 19 (79.2)

Ā 

Denosumab (Prolia)

0 (0)

3 [17]

1 [11]

4 [11]

Ā 

Teriparatide (Forsteo)

1 [10]

0 (0)

1 [11]

2 [5]

Ā 

Other types of drugs

1 [10]

3 [17]

3 [33]

7 [19]

Ā 

Vit D intakeā€“ Yes

12 (60)

26 (84)

12 (86)

50 (77)

Ā 

Calcium intakeā€“ Yes

12 (60)

14 [45]

10 (72)

36 (55)

Ā 

Oral Conditions

Enrollment numberā€“ n (%)

9 [36]

10 [44]

5 [20]

24 (100)

Ā 

DI (Yes)ā€“ n (%)

2 [22]

5 [13]

1 [20]

8 [33]

Ā 

Molar classificationā€“ n (%)

Ā 

Cl

6 (67)

3 [30]

0 (0)

9 [38]

Ā 

Clll

2 [22]

4 [40]

3 (60)

9 [38]

Ā 

Cll and neglected*

1 [11]

3 [30]

2 [40]

6 [24]

Ā 

Anterior open biteā€“ n (%) Yes

0 (0)

2 [20]

3 (60)

5 [21]

Ā 

Posterior open biteā€“ n (%) Yes

1 [11]

0 (0)

3 (60)

4 [17]

Ā 

Anterior crossbiteā€“ n (%) Yes

0 (0)

3 [30]

3 (60)

6 [25]

Ā 

Posterior crossbiteā€“ n (%) Yes

1 [11]

3 [30]

3 (60)

7 [29]

Ā 
  1. Statistical tests between categorical variables and OI types (mild, moderate, and severe): chi-square test for contingency tables; Kruskalā€’Wallis test for age; and oral survey with OI type as the independent variable. *Neglected: missing molars or removable dentures