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Table 2 Echocardiographic parameters in osteogenesis imperfecta patients and controls

From: Echocardiographic abnormalities and joint hypermobility in Chinese patients with Osteogenesis imperfecta

 

OI- Juveniles

Control- Juveniles

P

OI-Adults

Control-Adults

P

AD (cm)

21.44 ± 4.49

21.94 ± 2.82

0.606

26.03 ± 2.40

27.28 ± 2.30

0.038

AD/BSA

18.47 ± 4.56

15.36 ± 2.98

0.003

17.72 ± 2.25

15.85 ± 1.62

0.001

LAD (cm)

28.96 ± 6.89

28.28 ± 4.64

0.647

31.78 ± 3.20

31.26 ± 4.27

0.603

LAD/BSA

24.63 ± 5.41

19.69 ± 3.73

<0.001

21.63 ± 2.88

18.09 ± 2.17

<0.001

IVST (cm)

6.68 ± 1.41

7.20 ± 1.20

0.072

8.13 ± 1.32

8.24 ± 1.17

0.723

IVST/BSA

5.81 ± 1.66

5.02 ± 1.01

0.033

5.51 ± 0.92

4.79 ± 0.76

0.001

LVPWT (cm)

6.52 ± 1.44

7.13 ± 1.10

0.073

7.83 ± 1.14

7.96 ± 0.99

0.627

LVPWT/BSA

5.65 ± 1.59

4.99 ± 1.07

0.075

5.28 ± 0.93

4.62 ± 0.63

0.006

LVEDd (cm)

41.42 ± 7.83

42.59 ± 5.24

0.495

43.30 ± 3.55

44.44 ± 3.55

0.208

LVEDd/BSA

35.83 ± 9.22

29.83 ± 5.79

0.005

29.49 ± 3.66

25.84 ± 2.68

<0.001

LVESd (cm)

26.92 ± 4.99

27.51 ± 3.75

0.535

28.04 ± 2.64

28.62 ± 2.72

0.398

LVESd/BSA

23.32 ± 6.17

19.26 ± 3.91

0.005

19.10 ± 2.57

16.64 ± 1.93

<0.001

LVEF

62.91 ± 9.45

64.96 ± 3.68

0.910

64.43 ± 2.93

64.96 ± 3.83

0.571

LVEF/BSA

33.95 ± 15.95

47.01 ± 15.15

0.318

43.55 ± 5.02

37.98 ± 5.23

<0.001

FS

35.52 ± 3.49

35.43 ± 2.95

0.910

35.27 ± 2.42

35.46 ± 3.19

0.796

FS/BSA

33.95 ± 15.95

25.63 ± 8.28

0.024

24.06 ± 3.08

20.73 ± 3.15

<0.001

LVM (g)

84.93 ± 44.33

93.18 ± 32.47

0.413

102.04 ± 30.81

188.35 ± 39.06

<0.001

LVM/BSA

42.47 ± 22.16

46.59 ± 16.24

0.413

68.71 ± 19.61

108.32 ± 17.41

<0.001

  1. Abbreviations OI: osteogenesis imperfecta; BSA: body surface area; AD: aorta diameter; LAD: left atrium diameter; IVST: interventricular septum thickness; LVPWT: left ventricular posterior wall thickness; LVEDd: left ventricular end-diastolic diameter; LVESd: left ventricular end-systolic diameter; LVEF: left ventricular ejection fraction; FS: fractional shortening; LVM: Left ventricular mass. Bold P values indicate significance.