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Table 2 Liver histology score

From: Clinical symptoms, biochemistry, and liver histology during the native liver period of progressive familial intrahepatic cholestasis type 2

Patient number

Init

End

Age

Sampling

Score

Age

Sampling

Score

Cholestasis

Parenchymal change

Portal tract change

Fibrosis

Cholestasis

Parenchymal change

Portal tract change

Fibrosis

C01

3Y

Biopsy

2

4

3

3

4Y9M

Explant

8

9

6

7

C02

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

C03

0Y6M

Biopsy

3

5

3

1

1Y11M

Explant

8

11

6

7

C04

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

C05

NA

NA

NA

NA

NA

NA

0Y9M

Explant

8

10

4

5

C06

0Y7M

Biopsy

7

9

3

4

0Y9M

Explant

8

10

5

6

C07

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

C08

NA

NA

NA

NA

NA

NA

0Y9M

Explant

5

6

4

3

C09

0Y4M

Biopsy

7

9

5

7

NA

NA

NA

NA

NA

NA

C10

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

C11

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

NA

C12

0Y4M

Biopsy

3

10

4

3

0Y4M

Explant

5

11

5

5

T01

0Y4M

Biopsy

3

1

7

4

5Y0M

Biopsy

3

1

1

4

T02

0Y3M

Biopsy

6

5

3

3

4Y0M

Biopsy

2

3

2

3

  1. M month, NA not available, Y year