Table 1 Study participant demographics

Study population (n)

105

77

13

15

-

Sex (% female)

52.8%

(n = 55)

51.3%

(n = 39)

53.8%

(n = 7)

55.5%

(n = 9)

0.98^{^}

Age (years)

14.6 ± 9.1

[1–32]

(n = 105)

11.7 ± 8.1

[1–30]

(n = 77)

20.6 ± 8.4

[3–32]

(n = 13)

24.1 ± 8.1

[16–31}

(n = 15)

0.0001^{^}

% Forced vital capacity

61.9 ± 18.8

[35–94]

(n = 47)

55.9 ± 16.4

[35–92]

(n = 37)

82.8 ± 11.0

[62–94]

(n = 10)

-

0.001^†

IgA (% deficient)

53%

(n = 47)

61%

(n = 41)

0%

(n = 6)

-

0.004^†

AFP (ng/ml)

201.3 ± 205.2

[2.7-1212.5]

(n = 82)

227.1 ± 209.6

[21-1212.5]

(n = 71)

41.8 ± 45.8

[2.7-154.7]

(n = 11)

-

0.005^†