Table 4 Need for ventilation
From: RegistrAME: the Spanish self-reported patient registry of spinal muscular atrophy
Variable | SMA type 1 | SMA type 2 | SMA type 3 | SMA type 4 | Total N = 295 N (%) | |
|---|---|---|---|---|---|---|
N = 65 | N = 143 | N = 85 | N = 2 | |||
N (%) | N (%) | N (%) | N (%) | |||
Invasive Ventilation | Yes, part of the day* | 8 (12.31%) | 1 (0.7%) | 0 (0%) | 0 (0%) | 9 (3.05%) |
Yes, all day | 5 (7.69%) | 0 (0%) | 0 (0%) | 0 (0%) | 5 (1.69%) | |
Noninvasive Ventilation | Yes, part of the day* | 37 (56.92%) | 78 (54.55%) | 7 (8.24%) | 0 (0%) | 122 (41.36%) |
Yes, all day | 1 (1.54%) | 0 (0%) | 0 (0%) | 0 (0%) | 1 (0.34%) | |
Never use any type of ventilation | 14 (21.54%) | 64 (45.45%) | 78 (91.76%) | 2 (100%) | 158 (53.56%) | |
Mean (SD) / n (%) | Median (1st, 3rd Q.) | |||||
Age of onset of invasive ventilation | 1.92 (3.41) | 15 (-) | - | 2.85 (4.79) | ||
0.83 (0.5, 1.17) | 15 (15, 15) | - | 0.88 (0.52, 1.79) | |||
Age of onset of noninvasive ventilation | 1.22 (1.6) | 11.58 (11.83) | 33.86 (18.61) | 9.63 (12.83) | ||
0.5 (0.33, 1.19) | 8 (3, 14) | 35 (26.5, 43.5) | 4.5 (1.31, 12) | |||