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Table 2 Human ECM Degradation qPCR Array

From: Dysregulation of extracellular matrix and Lysyl Oxidase in Ehlers-Danlos syndrome type IV skin fibroblasts

QPCR Summary Fold Change vEDS vs. WT

mRNA Target Symbol

Fold Change

MMP1

6.962342489

COL11A1

5.104343495

COL4A1

3.584455047

COL6A3

3.145581688

BGN

2.375276316

COL6A1

2.340336341

DMD

2.169633723

BMP4

2.149695757

ADAMTS4

2.092166273

FN1

1.92169555

GAPDH

1.889499158

COL7A1

1.721856545

COL18A1

1.625125205

PCOLCE

1.553823988

LAMB1

1.426785625

LAMA2

1.423258809

BMP1

1.33745086

LTBP2

1.257522633

LAMB2

1.234407337

COL1A1

1.219734013

CTSS

1.217699027

COL5A1

1.214205762

ADAM15

1.178961982

LAMA5

1.178854439

CAPN2

1.056289346

COL1A2

1.055825812

MMP2

1.038080068

CAST

0.9890324018

CEACAM8

0.9820693563

COL3A1

0.9718347934

TIMP2

0.9652007999

NONO

0.904317416

SERPINH1

0.853765881

ADAMTS5

0.8496761203

NCSTN

0.845181235

SPP1

0.8239319581

HTRA1

0.8237772923

LDHA

0.7774874025

CAPN3

0.7771390241

MMP14

0.7744722796

ADAM17

0.7710375361

CD44

0.7684384603

PPIH

0.7526935221

A2M

0.7406034906

COL5A2

0.7331314954

CAPN1

0.7302497675

ADAM10

0.7239983982

CASP3

0.7123353739

LAMC2

0.7114149282

NID1

0.7039386135

LUM

0.6820986187

SPARC

0.662943773

DCN

0.6558146898

TIMP1

0.611488994

HSPG2

0.6026032143

LAMC1

0.5129034627

PSEN1

0.5027737176

COL14A1

0.4827554669

ADAM12

0.454108097

VCAN

0.440161167

LAMA1

0.4186142104

LAMA3

0.2952541361

PLG

0.2678408736

COL4A5

0.2537784676

COL4A3

0.2223562489

NTN4

0.2131865271

PPC

0.2114188166

FBN1

0.1730133034

MMP12

0.1668759578

LAMB3

0.1646102454

CAPN10

0.1454183852

ADAMTS1

0.1435083107

CAPN9

0.1182502418

ACAN

0.1111956171

MMP3

0.01051777272