Table 1 Prevalence of RD cases as of December 31, 2019 and crude mortality rates (year 2019) by gender and age group
From: Estimating mortality in rare diseases using a population-based registry, 2002 through 2019
Prevalence per 10,000—as of December 31, 2019 | Mortality rate per 100,000—Year 2019 | |||
|---|---|---|---|---|
95% CI | 95% CI | |||
Total | 62.93 | 62.23–63.63 | 8.87 | 8.03–9.70 |
Gender | ||||
Male | 59.41 | 58.44–60.38 | 8.66 | 7.48–9.84 |
Female | 66.31 | 65.30–67.31 | 9.06 | 7.88–10.24 |
Age | ||||
0–12 months | 35.37 | 29.11–41.64 | 0.15* | 0.02*–0.28* |
1–4 years | 62.38 | 58.44–66.32 | 4.56 | 1.18–7.94 |
5–9 years | 81.94 | 78.18–85.70 | 1.36 | 0.00–2.89 |
10–14 years | 90.87 | 87.05–94.70 | 3.38 | 1.04–5.72 |
15–19 years | 76.82 | 73.28–80.36 | 0.43 | 0.00–1.26 |
20–29 years | 59.32 | 57.16–61.49 | 0.62 | 0.00–1.32 |
30–39 years | 52.24 | 50.32–54.16 | 1.11 | 0.22–1.99 |
40–49 years | 54.43 | 52.78–56.09 | 2.90 | 1.69–4.12 |
50–59 years | 63.31 | 61.57–65.05 | 5.02 | 3.47–6.58 |
60–69 years | 71.41 | 69.28–73.54 | 14.49 | 11.45–17.54 |
70–79 years | 69.08 | 66.77–71.39 | 28.34 | 23.65–33.04 |
80–89 years | 47.36 | 44.85–49.86 | 34.32 | 27.56–41.08 |
90 + years | 16.84 | 13.69–20.00 | 21.64 | 10.30–32.97 |