Long-term benefits of physical activity in adult patients with late onset Pompe disease: a retrospective cohort study with 10 years of follow-up

Table 5 Patient characteristics physically active 2011 training cohort (continued training) vs. physically active controls

	Physically active 2011 training cohort (n = 9)	Physically active controls (n = 7)	p value
Age (y)	52.0 [45.0;66.0]	50.0 [39.0;73.0]	.364
Male sex n (%)	6 (67%)	5 (71%)	.838
BMI	23.7 [20.0;33.0]	25.9 [23.1;28.3]	.201
Disease duration (y)	17.0 [13.0;31.0]	13.0 [8.0;20.0]	.086
ERT duration (y)	13.0 [11.0;15.0]	11.0 [7.0;15.0]	.281
Ambulation aid n (%)	2 (22%)	2 (29%)	.771
	2 walking stick	1 rolling walker
	2 walking stick	1 partial wheelchair
Ventilator support n (%)*	2 (22%)	2 (29%)	.771

All values, if not stated otherwise, are presented as a median with a minimum and maximum range
*Non-invasive overnight ventilator support; Chi-square test for proportions (Asymptotic significance (2 sided)) and Mann–Whitney U test (Exact significance 2-tailed) for continuous unpaired data are used
BMI Body mass index, ERT enzyme replacement therapy

ISSN: 1750-1172