Physically active (n = 16) | Physically inactive (n = 13) | p value | |
---|---|---|---|
Age (y) | 52.0 [39.0;73.0] | 50.0 [36.0;75.0] | .821 |
Male sex n (%) | 11 (69%) | 6 (46%) | .219 |
BMI | 24.8 [22.0;33.0] | 26.7 [20.6;34.9] | .722 |
Disease duration (y) | 16.0 [8.0;31.0] | 17.0 [7.0;41.0] | .523 |
ERT duration (y) | 12.5 [7.0;15.0] | 12.0 [7.0;14.0] | .533 |
Ambulation aid n (%) | 4 (25%) | 5 (38%) | .436 |
2 walking stick | 2 walking stick | ||
1 rolling walker | 1 rolling walker | ||
1 partial wheelchair | 2 partial wheelchair | ||
Ventilator support n (%)* | 4 (25%) | 5 (38%) | .436 |