Skip to main content

Table 3 Baseline characteristics of 146 PiSZ patients split according to CT scan findings

From: The prevalence of bronchiectasis in patients with alpha-1 antitrypsin deficiency: initial report of EARCO

CT scan performed

(% of pts)

146 (62.1%)

Pack years

FEV1% predicted

Pre-bronchodilator

KCO % predicted

Bx alone

Current smoker

Ex-smoker

Never

17 (11.6%)

2 (11.8%)

6 (35.3%)

9 (52.9%)

ND

16.5 (14.0%)

0

ND

104.3 (22.7) n = 5

89.7 (14.4) n = 7

ND

96.1 (13.3) n = 6

93.1 (11.4) n = 7

Emphysema alone

Current smoker

Ex-smoker

Never

47 (32.2%)

10 (21.2%)

31 (66.0%)

6 (12.8%)

32.6 (23.7)

41.3 (24.7)

0

95.1 (21.1) n = 9

88.2 (21.2) n = 22

ND

72.7 (20.3) n = 8

64.7 (23.5) n = 26

72.4 (31.5) n = 5

Emphysema + Bx

Current smoker

Ex-smoker

Never

21 (14.4%)

3 (14.2%)

17 (81.0%)

1 (4.8%)

ND

38.2 (36.7)

0

ND

76.8 (34.5) n = 12

ND

ND

68.5 (20.3) n = 15

ND

Normal CT scan

Current smoker

Ex-smoker

Never

61 (41.8%)

2

20

39

ND

12.1 (10.4)

0

ND

94.1 (20.2) n = 15

101.6 (18.6) n = 29

ND

99.5 (17.0) n = 15

90.7 (13.8) n = 30

  1. Data is shown as number and % in parentheses or mean and SD