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Table 2 Baseline characteristics of 418 PiZZ patients split according to CT scan findings

From: The prevalence of bronchiectasis in patients with alpha-1 antitrypsin deficiency: initial report of EARCO

 

Bronchiectasis alone

Emphysema alone

Bronchiectasis plus Emphysema

Normal CT scan

Total, n

38

190

113

77

Age, years: Mean (SD)

57.2 (10.2)

58.8 (9.9)

61.1 (11.0)

46.2 (14.0)

Male, n (%)

11 (28.9%)

112 (58.9%)

59 (52.2%)

36 (46.8%)

Smoking, n (%)

    

 Current

0

4 (2.1%)

0

2 (2.6%)

 Ex-smoker

12 (31.6%)

140 (73.7%)

77 (68.1%)

20 (26.0%)

 Never

26 (68.4%)

46 (24.2%)

36 (31.9%)

54 (70.1%)

 Unknown

0

0

0

1 (1.3%)

Pack years: Mean (SD)

14.0 (15.7)

20.8 (13.6)

17.1 (10.1)

9.35 (8.8)

 Mean FEV1%

Post BD (SD)

98.3% (18.0)

56.2% (24.3)

59.6% (27.5)

92.6% (20.2)

 Mean Kco % (SD)

83.1% (17.8)

54.7% (18.9)

65.1% (19.1)

90% (16.9)