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Table 1 Baseline characteristics

From: Tafamidis decreased cardiac amyloidosis deposition in patients with Ala97Ser hereditary transthyretin cardiomyopathy: a 12-month follow-up cohort study

 

ATTR-CM (N = 14)

Control (N = 17)

P value

Age, year

62.1 ± 4.9

60.7 ± 15.4

0.914

Male

13 (93%)

11 (65%)

0.062

Body height, cm

166.6 ± 6.6

166.5 ± 9.2

0.804

Body weight, kg

57.9 ± 11.0

69.6 ± 12.0

0.012

Body mass index, kg/m2

20.8 ± 3.6

25.1 ± 3.8

0.006

Diabetes Mellitus

0 (0%)

3 (18%)

0.232

Hypertension

1 (7%)

5 (3%)

0.185

Coronary artery disease

2 (14%)

5 (29%)

0.412

Atrial fibrillation

1 (7%)

0 (0%)

0.452

Pacemaker use

2 (14%)

0 (0%)

0.196

NYHA Fc I

1 (7%)

17 (100%)

< 0.001

NYHA Fc II

12 (86%)

0 (0%)

NYHA Fc III

1 (7%)

0 (0%)

Biochemistry

 Creatinine, mg/dL

0.8 ± 0.2

0.9 ± 0.4

0.310

 Triglyceride, mg/dL

74.5 ± 27.0

109.9 ± 38.4

0.015

 Total cholesterol, mg/dL

173.9 ± 31.6

188.1 ± 38.6

0.403

 Fasting glucose, mg/dL

83.5 ± 15.0

100.1 ± 15.5

0.003

 Albumin, g/dL

4.1 ± 0.2

-

 

 Prealbumin*, mg/dL

27.1 ± 9.1

-

 

 NT-ProBNP, pg/dL

2078.1 ± 3886.3

90.2 ± 73.1

< 0.001

 LogNT-proBNP

3.0 ± 0.5

1.8 ± 0.4

< 0.001

Echocardiography

 IVSD, mm

15.4 ± 2.5

12.0 ± 1.4

0.001

 LVPWD, mm

14.8 ± 2.1

9.9 ± 1.2

< 0.001

 LVEDD, mm

45.2 ± 3.7

49.4 ± 4.2

0.029

 LVESD, mm

31.6 ± 4.8

30.8 ± 5.2

0.616

 LVEF, %

56.6 ± 11.7

66.4 ± 9.7

0.238

 LA diameter, mm

40.5 ± 4.5

40.4 ± 3.6

0.714

  1. *Prealbumin only available in 6 patients (5 in ECV improved group and 1 in ECV non-improved group)
  2. Abbreviation: NYHA = New York Heart Association functional classification; NT-ProBNP = N-terminal pro-B-type natriuretic peptide; IVSD = interventricular septal diameter; LVPWD = Left ventricular posterior wall diameter; LVEDD = left ventricular end-diastolic diameter; LVESD = left ventricle end-systolic diameter; LVEF = left ventricular ejection fraction; LA diameter = left atrial diameter