From: Thalassemia and hemoglobinopathy prevalence in a community-based sample in Sylhet, Bangladesh
Characteristics | Non-pregnant women | Pregnant women | Children (6–37 months) | ||||||
---|---|---|---|---|---|---|---|---|---|
n | Hemoglobin (g/dl) | Anemiaa | n | Hemoglobin (g/dl) | Anemiaa | n | Hemoglobin (g/dl) | Anemiaa | |
Mean (SD) | Freq. (%) | Mean (SD) | Freq. (%) | Mean (SD) | Freq. (%) | ||||
Total population | 768 | 12.4 (1.2) | 244 (31.7) | 132 | 11.5 (1.2) | 31 (23.5) | 395 | 10.9 (1.3) | 195 (49.4) |
Any inherited blood disorders | 87 | 12.1 (1.2) | 37 (42.5) | 15 | 10.8 (1.4) | 6 (40.0) | 41 | 10.5 (1.3) | 25 (61.0) |
Alpha thalassemia | |||||||||
Any | 53 | 12.2 (1.3) | 21 (39.6) | 9 | 11.2 (1.3) | 3 (33.3) | 21 | 10.8 (1.2) | 10 (47.6) |
Minima (aa/−a) | 51 | 12.2 (1.3) | 20 (39.2) | 8 | 11.4 (1.3) | 2 (25.0) | 21 | 10.8 (1.2) | 10 (47.6) |
a3.7deletion | 48 | 12.2 (1.3) | 18 (37.5) | 8 | 11.4 (1.3) | 2 (25.0) | 19 | 10.8 (1.2) | 9 (47.4) |
a4.2deletion | 3 | 11.6 (0.8) | 2 (66.7) | 0 | – | – | 2 | 10.6 (1.3) | 1 (50.0) |
Minor (aa/− or a−/a−) | |||||||||
a3.7deletions | 1 | 11 | 1 (100.0) | 1 | 9.8 | 1 (100.0) | 0 | – | – |
Hemoglobin Constant Spring | 1 | 13.3 | 0 (0.0) | 0 | – | – | 0 | – | – |
Triplicate alpha-globin genes (> 5) | 20 | 12.7 (1.3) | 7 (35.0) | 3 | 12.8 (0.4) | 0 (0.0) | 14 | 10.7 (1.1) | 7 (50.0) |
aaaanti3.7 | 18 | 12.7 (1.3) | 6 (33.3) | 3 | 12.8 (0.4) | 0 (0.0) | 14 | 10.7 (1.1) | 7 (50.0) |
aaaanti4.2 | 1 | 12.8 | 0 (0.0) | 0 | – | – | 0 | – | – |
Unknown | 1 | 11.2 | 1 (100.0) | 0 | – | – | 0 | – | – |
Beta thalassemia | |||||||||
Minor (HbA2 < 3.5%) | 13 | 11.4 (1.1) | 9 (69.2) | 2 | 9.1 (0.4) | 2 (100.0) | 9 | 10.5 (1.3) | 7 (77.8) |
Hemoglobin E | 23 | 12.1 (1.1) | 8 (34.8) | 4 | 10.8 (1.5) | 1 (25.0) | 7 | 10.4 (0.9) | 5 (71.4) |
Hemoglobin D | 1 | 13.8 (0.0) | 0 (0.0) | 0 | – | – | 2 | 11.3 (0.7) | 1 (50.0) |
Hemoglobin S | 1 | 13.7 (0.0) | 0 (0.0) | 0 | – | – | 0 | – | – |
Hemoglobin X (unable to identify) | 0 | 0 (0.0) | 0 (0.0) | 0 | – | – | 5 | 9.3 (2.0) | 4 (80.0) |