Table 2 Common conditions and procedures/services related to XLMTM in the overall XLMTM population with a diagnosis of congenital myopathy
Percent of patients (N = 192) | |
|---|---|
Conditions | |
Respiratory distress, failure, arrest | 82% |
Acute | 54% |
Chronic | 96% |
Acute and chronic | 46% |
Feeding difficulties and related problems | 81% |
Gastrostomy* | 69% |
Tracheostomy* | 64% |
Ventilator use or dependence | 61% |
Other myopathies | 77% |
Scoliosis | 42% |
Liver disorders | 33% |
Wheelchair dependence | 21% |
Procedures/services | |
Ventilation management or equipment | 82% |
Feeding support | 72% |
Critical or emergency care | 71% |
Tracheostomy (procedure or supplies)* | 62% |
Wheelchair equipment | 56% |
Gastrostomy (procedure)* | 52% |
Hospital/Inpatient care | 46% |
Occupational Therapy or Phyiscal Therapy | 49% |
Home care | 35% |