Characteristic | TAZPOWER patients (n = 8) | Natural history controls (n = 19) |
---|---|---|
Age at baseline, years | ||
 Mean (SD) | 18.3 (5.02) | 21.0 (5.46) |
 Range | 12.9 –28.7 | 12.0 – 32.6 |
Height at baseline, cm | ||
 Mean (SD) | 166.6 (12.43) | 168.6 (14.25) |
 Range | 152.5 – 180.8 | 121.3 – 186.0 |
Baseline 6MWT | ||
 Mean (SD) | 381.875 (64.1837) | 394.879 (75.2197) |
 Range | 313.00 –495.00 | 267.00 –536.45 |