From: Hepatic glycogen storage diseases type 0, VI and IX: description of an italian cohort
First visit | Last visit | p value | |||
---|---|---|---|---|---|
Median | IQR | Median | IQR | ||
Carbohydrate% | 58.4 | 10.1 | 57.1 | 11.1 | ns |
Lipid% | 27.8 | 4.8 | 25.0 | 8.5 | ns |
Protein% | 14.0 | 4.7 | 19.1 | 6.4 | < 0.001 |
Carbohydrate%/RDA ratio | 1.1 | 0.2 | 1.1 | 0.2 | ns |
Lipid%/RDA ratio | 0.8 | 0.3 | 0.9 | 0.3 | ns |
Protein%/RDA ratio | 1.2 | 0.7 | 1.0 | 0.4 | ns |
Protein (g/kg) | 2.9 | 1.7 | 2.3 | 1.2 | ns |
Protein (g/kg)/RDA ratio | 2.8 | 1.6 | 2.3 | 1.2 | ns |
Total calories | 1079.0 | 312.3 | 1686.7 | 574.3 | < 0.001 |
Calories/RDA ratio | 1.0 | 0.4 | 0.8 | 0.3 | < 0.05 |
Calories/kg | 76.2 | 37.5 | 54.3 | 45.0 | < 0.001 |
Glucose mg/kg/min | 7.4 | 4.7 | 4.7 | 4.0 | < 0.01 |