Skip to main content

Table 3 Descriptive skeletal muscle structural and functional characteristics, ordered by V̇O2peak (from highest to lowest)

From: Aerobic capacity and skeletal muscle characteristics in glycogen storage disease IIIa: an observational study

Participant

Functional characteristics

Structural characteristics

MVC (Nm)

Predicted MVC (Nm)

Percentage achieved (%)

MVC/BM (Nm/kg)

Predicted MVC/BM (Nm/kg)

Percentage achieved (%)

RTD 0–200 ms (Nm∙s)

Vastus Lateralis Muscle Volume (cm3)

Vastus Lateralis PCSA (cm2)

Muscle Quality (Nm∙cm2)

1

267

281

95

3.28

2.67

123

975

726

126

2.13

2

225

210

107

3.07

2.87

107

–

544

81

2.77

3

309

302

102

3.83

3.75

102

965

940

139

2.23

4

47

226

21

0.68

3.25

21

214

273

36

1.32

5

56

198

28

0.64

2.44

26

–

323

48

1.17

6

43

174

25

0.54

2.21

24

192

393

54

0.79

7

77

339

23

0.69

3.03

23

328

419

54

1.44

Mean (SD)

146 (116)

247 (61)

57 (42)

 

2.89 (0.52)

61 (47)

 

516 (240)

77 (40)

1.60 (0.70)

Median (IQ range)

  

28 (80)

1.82 (2.64)

 

26 (84)

328 (767)

   
  1. MVC maximum voluntary contraction, BM body mass, RTD rate of torque development, PCSA physiological cross-sectional area
Back to article page

Orphanet Journal of Rare Diseases

ISSN: 1750-1172