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Table 2 Cardio-respiratory properties, ordered by V̇O2 peak

From: Aerobic capacity and skeletal muscle characteristics in glycogen storage disease IIIa: an observational study

Participant

   

Cardio-respiratory characteristics

PA characteristics (min/day)

Ramp duration (min:s)

V̇O2peak (ml/kg/min)

V̇O2peak (% of predicted)

Peak WR (W)

Peak WR (% of Predicted)

Peak V̇E (L/min)

V̇E (% of Predicted)

Peak Heart Rate (BPM)

Heart rate (% of Predicted)

Peak RER

SB

LIPA

MPA

VPA

1

10:40

27.1

67

159

63

53

29

179

93

0.97

410

313

227

0

2

09:49

25.9

91

146

82

56

33

169

88

0.99

650

170

129

11

3

10:16

25.7

63

153

52

63

27

163

84

0.91

637

200

124

0

4

03:39

15.0

46

54

25

27

18

130

76

0.88

669

218

73

0

5

05:36

9.4

45

41

28

16

16

139

82

0.81

448

459

53

0

6

03:43

8.7

37

35

30

21

21

121

69

0.93

640

163

157

0

7

02:32

7.0

22

25

9

22

11

102

54

0.85

678

228

34

0

Mean (SD)

06:36 (03:32)

17.0 (9.0)

53 (24)

  

37 (20)

22 (8)

143 (28)

78 (13)

0.91 (0.06)

590 (112)

250 (105)

114 (67)

1.6 (0)

Median (IQ range)

   

54 (118)

30 (38)

     

640 (221)

  

0 (0)

  1. V̇O2, oxygen utilisation; WR, work rate, V̇E, minute ventilation; RER, respiratory exchange ratio; PA, physical activity; SB, sedentary behaviour; LIPA, Light-intensity physical activity; MPA, moderate-intensity physical activity; HPA, High-intensity physical activity
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Orphanet Journal of Rare Diseases

ISSN: 1750-1172