Table 1 Baseline characteristics of patients with severe haemophilia B in CHESS II
All patients (n = 75) | SHL (n = 42) | EHL (n = 33) | |
|---|---|---|---|
Age, mean (SD) | 36.2 (15.97) | 33.7 (14.26) | 39.3 (17.66) |
Weight, kg, mean (SD) | 77.3 (11.07) | 74.0 (11.58) | 79.9 (10.06) |
Country, n (%) | |||
UK | 22 (29) | 15 (36) | 7 (21) |
Italy | 17 (23) | 11 (26) | 6 (18) |
Spain | 15 (20) | 9 (21) | 6 (18) |
France | 11 (15) | 4 (10) | 7 (21) |
Germany | 10 (13) | 3 (7) | 7 (21) |
Medical history, n (%) | |||
Anxiety | 9 (12) | 5 (12) | 4 (12) |
Depression | 5 (7) | 4 (10) | 1 (3) |
HIV | 1 (1) | 0 | 1 (3) |
Hepatitis B | 4 (5) | 3 (7) | 1 (3) |
Hepatitis C | 9 (12) | 4 (10) | 5 (15) |
FIX prophylaxis treatment, n (%) | |||
EHL | 33 (44) | – | 33 (100) |
SHL | 42 (56) | 42 (100) | – |
Primary FIX prophylaxis, n (%) | 57 (76) | 29 (69) | 28 (85) |
Secondary FIX prophylaxis, n (%) | 18 (24) | 13 (31) | 5 (15) |