Fig. 2

Mean cystine levels. This figure shows the mean cystine levels of all patients, including standard deviations, when taking IR-cysteamine (Cystagon®, blue) as well as DR-cysteamine (Procysbi®, orange) over a period of 360 min, 720 min respectively. Initially, patients’ cystine levels are similar under both formulas. Mean cystine levels reach their trough value after 90 min under IR-cysteamine and after 180 min under DR-cysteamine. Both drugs lead to the target value of cystine under 0.5 nmol cystine/mg protein