From: Microcephalic osteodysplastic primordial dwarfism type II is associated with global vascular disease
% (n) | Mean age +/− SD (years) | Median age (min–max) (years) | ||
---|---|---|---|---|
Consented | Registry | 100% (47) | 15.96 +/− 9.5 | 14 (3–41) |
Survey | 81% (38) | 16.03 +/− 10.1 | 14 (3–41) | |
Completed | 51% (24) | 19.7 +/− 9.8 | 18.5 (3–41) | |
Partially | 13% (6) | 14.3 +/− 9.9 | 12 (5–28) | |
Not completed | 17% (8) | 6.3 +/− 3.8 | 5 (3–14) | |
Sex | Female | 47% (22) | 16.1 +/− 10.0 | 13.5 (3–37) |
Male | 53% (25) | 15.8 +/− 9.1 | 14 (3–41) | |
Status | ||||
Living | Current age | 72% (34) | 14.1 +/− 8.9 | 13 (3–37) |
Deceased | At age | 28% (13) | 20.8 +/− 9.6 | 22 (7–41) |
Race | n | |||
White | 35 | |||
Asian | 5 | |||
Black | 2 | |||
Hispanic | 2 | |||
Aboriginal | 1 | |||
Native Hawaiian | 1 | |||
Unknown | 1 | |||
Country | ||||
USA | 32 | |||
UK | 5 | |||
Australia | 2 | |||
Canada | 2 | |||
Ireland | 2 | |||
Netherlands | 2 | |||
Guatemala | 1 | |||
New Zealand | 1 |