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Table 1 ACR–EULAR classification criteria for systemic sclerosis

From: French recommendations for the management of systemic sclerosis

Domain

Criteria*

Score#

Cutaneous thickening (only consider the highest score)

Cutaneous thickening of the fingers extending beyond the MCP joints

9

Swollen fingers

2

Symptoms of the fingers not extending beyond the MCP joints

4

Pulp lesions (only consider the highest score)

Digital pulp ulcers

2

Depressed scars

3

Telangiectasias

 

2

Capillaroscopic anomalies

 

2

Pulmonary damage

PAH and/or pulmonary fibrosis

2

Raynaud’s phenomenon

 

3

SSc-specific antibodies

Anti-topoisomerase I

3

Anticentromere antibodies

Anti-RNA polymerase III

  1. RNA ribonucleic acid, MCP metacarpophalangeal, SSc systemic sclerosis
  2. *This criterion can be included if appearing at any time during the clinical history
  3. #The weight of each item present must be summed to obtain the total score. A score of 9 or more permits classifying patients as having SSc