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Table 1 Baseline characteristics of patients with lymphangioleiomyomatosis

From: Pregnancy after the diagnosis of lymphangioleiomyomatosis (LAM)

Characteristics Numbers (%)
Patients 30
Age of diagnosis (years) 29.4 ± 4.9
Diagnosis  
 TSC-LAM 3 (10.0)
 Sporadic-LAM 27 (90.0)
Complications  
 Renal AML 11 (36.7)
 History of pneumothorax 14 (56.7)
 History of chylothorax 7 (23.3)
Pulmonary function testinga  
 FEV1 (L) 2.17 ± 0.77
 FEV1/pred (%) 73.78 ± 25.66
 FVC (L) 3.19 ± 0.57
 FVC/pred (%) 93.70 ± 16.58
 FEV1/FVC (%) 66.80 ± 19.19
 DLco (mmol/min/kPa) 5.27 ± 2.29
 DLco pred (%) 48.31 ± 21.13
 6-min walking distance (m)b 509.43 ± 68.90
 Total score on St. George’s Respiratory Questionnairec 32.91 ± 19.17
 History of pregnancy before diagnosis of LAM 18 (60.0)
 Patients with live birth 16 (53.3)
 Patients with spontaneous abortion 0
 Patients with pneumothorax during pregnancy 2 (6.7)
  1. Data with a normal distribution are presented as the means ± standard deviation (SD), and data with a nonnormal distribution are reported as the median (Q1, Q3)
  2. AML angiomyolipoma, DLco diffusing capacity for carbon monoxide, FEV1 forced expiratory volume in 1 s, FVC forced vital capacity, LAM lymphangioleiomyomatosis, TSC tuberous sclerosis complex
  3. aSample size for pulmonary function testing was 21
  4. bSample size for 6-min walking testing was 21
  5. cSample size for St. George’s respiratory questionnaire was 22