Variable
| |
N = 22
|
---|
Age
|
Years
|
12.2 (8.5–20.9)a
|
Gender
|
Male
|
16 (72.7%)b
|
Onset of symptoms
|
Months
|
12.0 (6.0–12.0)a
|
Disease duration (since diagnosis)
|
Years
|
7.1 (4.4–13.1)a
|
Regular intravenous immunoglobulin
|
Yes
|
12 (54.5%)b
|
Pulmonar associated disease
|
Yes
|
3 (13.6%)b
|
Prophylactic antibiotic
|
Yes
|
5 (22.7%)b
|
Oral multivitamins
|
Yes
|
17 (77.3%)b
|
Family history of early cardiovascular disease
|
Yes
|
14 (63.6%)b
|
Alanine aminotransferase
|
> 40 U/L
|
5 (22.7%)b
|
AST/ALT
|
> 1
|
17 (77.3%)b
|
- AST/ALT aspartate aminotransferase/alanine aminotransferase
- aMedian (IQ25-75). IQ—interquartile interval
- bN (%)