Variable |  | N = 22 |
---|---|---|
Age | Years | 12.2 (8.5–20.9)a |
Gender | Male | 16 (72.7%)b |
Onset of symptoms | Months | 12.0 (6.0–12.0)a |
Disease duration (since diagnosis) | Years | 7.1 (4.4–13.1)a |
Regular intravenous immunoglobulin | Yes | 12 (54.5%)b |
Pulmonar associated disease | Yes | 3 (13.6%)b |
Prophylactic antibiotic | Yes | 5 (22.7%)b |
Oral multivitamins | Yes | 17 (77.3%)b |
Family history of early cardiovascular disease | Yes | 14 (63.6%)b |
Alanine aminotransferase |  > 40 U/L | 5 (22.7%)b |
AST/ALT |  > 1 | 17 (77.3%)b |