Table 1 Clinical features of conventional and fibrosarcomatous DFSP

Age at presentation (y)

 Mean ± SD

30.7 ± 14.4

35.4 ± 12.7

31.24 ± 14.23

 Median (range)

30.0 (0–66.0)

36.5 (12–57.0)

30.25 (0.0–66.0)

Age at diagnosis (y)

 Mean ± SD

37.3 ± 14.5

40.5 ± 10.3

37.69 ± 14.06

 Median (range)

37.0 (0.3–76.3)

43.1 (20.0–59.0)

37.5 (0.3–76.3)

The interval of diagnosis (y)

 Mean ± SD

6.5 ± 6.9

5.1 ± 6.5

6.3 ± 6.9

 Median (range)

4.3 (0–44.0)

1.8 (0.3–20.7)

4.0 (0–44.0)

Sex (male/female)

108/87

18/8

126/95

Size at presentation (cm)

 Mean ± SD

1.1 ± 1.0

1.0 ± 0.7

1.07 ± 1.05

 Median (range)

1.0 (0.2–10.0)

1.0 (0.1–3.0)

1.0 (0.1–10.0)

Size at diagnose

 Mean ± SD

2.7 ± 2.0

3.1 ± 1.7

2.8 ± 2.0

 Median (range)

2.0 (0.5–20.0)

3.0 (1.0–8.0)

2.50 (0.5–20.0)

Tumor growth

 Mean ± SD

1.7 ± 1.8

2.0 ± 1.7

0.9 ± 0.3

 Median (range)

1.0 (0–17.0)

1.7 (0–7.0)

1.5 (0–17.0)

Annual tumor growth

 Mean ± SD

0.9 ± 2.9

1.8 ± 2.4

0.97 ± 2.84

 Median (range)

0.3 (0–37.5)

0.7 (0–9.3)

0.3 (0–37.5)

Location

 Head-face-neck

21 (10.8%)

5 (19.2%)

26 (11.8%)

 Shoulder

11(5.6%)

2(7.7%)

13 (5.9%)

 Chest

51 (26.2%)

8 (30.8%)

59 (26.7%)

 Abdomen

49 (25.1%)

3 (11.5%)

52 (23.5%)

 Posterior thighs

40 (20.5%)

8(30.8%)

48 (21.7%)

 Upper extremity

11 (5.6%)

0 (0)

11 (5.0%)

 Lower extremity

12 (6.2%)

0 (0)

12 (5.4%)

Growth type

 Indolence

29 (14.9%)

1 (3.8%)

30 (13.6%)

 Gradually increasing

90 (46.2. %)

4 (15.4%)

94 (42.5%)

 Rapid enlargement

76 (38.9%)

21 (80.8%)

97 (43.9%)

Time to rapid enlargement (y)

 Mean ± SD

5.3 ± 6.5

0.9 ± 1.1

4.4 ± 6.0

 Median (range)

4.0 (0.1–41.0)

0.6 (0–5.0)

3.0 (0–41.0)

Cause

 Trauma

18

0

18

 Unknown

178 (91.3%)

26(100%)

204 (92.3%)

Pain

29

2

31

Metastasis

0

1

1

Recurrence

4

7

11

Follow-up

 Mean ± SD

4.8 ± 2.2

4.9 ± 1.7

4.8 ± 2.1

 Median (range)

4.6 (1.8–16.6)

4.6 (1.9–8.6)

4.6 (1.8–16.6)