From: Best practice guidelines in managing the craniofacial aspects of skeletal dysplasia
 | Strongly agree | Agree | Neutral | Disagree | Strongly disagree |
---|---|---|---|---|---|
1. As children with skeletal dysplasia are at increased risk of hearing loss, routine hearing screening should be performed at birth, at 12Â months of age and annually thereafter | 1 (8.3%) | 5 (41.7%) | 4 (33.3%) | 2 (16.7%) | 0 |
2. Children with skeletal dysplasia and acute otitis media should be treated with antibiotics | 1 (8.3%) | 5 (41.7%) | 3 (25%) | 3 (25%) | 0 |
3. Children with skeletal dysplasia and otitis media with effusion should be treated with antibiotics | 0 | 3 (25%) | 5 (41.7%) | 3 (25%) | 1 (8.3%) |
4. Adenoidectomy and/or tonsillectomy should be the first treatment for documented obstructive sleep apnea in children with skeletal dysplasia | 1 (8.3%) | 8 (66.7%) | 3 (25%) | 0 | 0 |
5. Children with skeletal dysplasia have a high risk of soft and hard palate abnormalities | 1 (8.3%) | 6 (50%) | 5 (41.7%) | 0 | 0 |
6. Supernumerary teeth and hypodontia are a frequent accompaniment of certain skeletal dysplasia | 4 (33.3%) | 5 (41.7%) | 2 (16.7%) | 1 (8.3%) | 0 |
7. Laryngomalacia and voice abnormalities are a frequent accompaniment s of certain skeletal dysplasia | 4 (33.3%) | 5 (41.7%) | 2 (16.7%) | 1 (8.3%) | 0 |
8. In neonates with diastrophic dysplasia and associated SLC26A2 conditions, auricular cystic swelling may progress to permanent deformities. This progression can be lessened by the use of incision and drainage techniques | 0 | 1 (8.3%) | 8 (66.7%) | 3 (25%) | 0 |
9. In neonates with diastrophic dysplasia and associated SLC26A2 conditions, auricular cystic swelling may progress to permanent deformities. This progression can be lessened by the use of compression molding techniques | 0 | 5 (41.7%) | 5 (50%) | 1 (8.3%) | 0 |
10. Prior to placement of tympanostomy tubes in children with achondroplasia, clinicians should look for otoscopic signs of a high jugular bulb | 5 (41.7%) | 4 (33.3%) | 3 (25%) | 0 | 0 |