Table 1 Statements that reached > 80% agreement in Round 1
From: Best practice guidelines in managing the craniofacial aspects of skeletal dysplasia
| Â | Strongly agree | Agree | Neutral | Disagree | Strongly disagree |
|---|---|---|---|---|---|
1. The mortality and morbidity risks for patients with skeletal dysplasia undergoing surgery are greater than the general population | 6(50%) | 6 (50%) | 0 | 0 | 0 |
2. Patients with skeletal dysplasia are more likely than the general population to have abnormal upper airway morphology and function, which can contribute to increased morbidity/mortality | 6(50%) | 6 (50%) | 0 | 0 | 0 |
3. Polysomnography should be considered in the pre-operative assessment of patients with skeletal dysplasia | 1 (83%) | 9 (75%) | 1 (83%) | 1 (83%) | 0 |
4. Routine evaluation and surveillance for hearing loss is indicated in patients with skeletal dysplasia | 3 (25%) | 9 (75%) | 0 | 0 | 0 |
5. As children with skeletal dysplasia are at increased risk for hearing loss, audiologic evaluation should be performed on any child with speech delay or a suspicion of hearing difficulties | 10(83.3%) | 2 (16.7%) | 0 | 0 | 0 |
6. Children with skeletal dysplasia and recurrent acute otitis media or with otitis media with effusion of any duration are at increased risk of speech, language, or learning problems | 4 (33.3%) | 7 (58.3%) | 1 (8.3%) | 0 | 0 |
7. Clinicians may perform tympanostomy tube insertion in children with skeletal dysplasia and unilateral or bilateral otitis media with effusion (OME) that is unlikely to resolve quickly, as reflected by a type B (flat) tympanogram or persistence of effusion for 3Â months or longer | 1 (8.3%) | 9 (75%) | 2 (16.7%) | 0 | 0 |
8. Patients with skeletal dysplasia who have snoring and restless sleep should have polysomnography to diagnose and measure severity of obstructive sleep apnea | 7 (58.3%) | 5 (41.7%) | 0 | 0 | 0 |
9. Children with skeletal dysplasia should undergo polysomnography before tonsillectomy or adenotonsillectomy is performed | 4 (33.3%) | 6 (50%) | 2 (16.7%) | 0 | 0 |
10. Children with skeletal dysplasia who undergo tonsillectomy and/or adenoidectomy for moderate or severe OSA should be monitored overnight for respiratory difficulties after surgery | 4 (33.3%) | 8 (66.7%) | 0 | 0 | 0 |
11. Children with skeletal dysplasia, especially those with hypognathia or midface hypoplasia have a high risk of malocclusion requiring orthodontic care | 2 (16.7%) | 8 (66.7%) | 2 (16.7%) | 0 | 0 |
12. Children with skeletal dysplasia should have routine dental care starting in early childhood | 6 (50%) | 6 (50%) | 0 | 0 | 0 |
13. Children with type II collagenopathy have a high risk of hearing loss and palate abnormalities | 9 (75%) | 1 (8.3%) | 2 (16.7%) | 0 | 0 |