From: Hereditary leiomyomatosis and renal cell carcinoma: a case series and literature review
RCC reported (n = 672) | |
Yes | 189 (28.1%) |
No | 353 (52.5%) |
NA | 130 (19.4%) |
RCC mean age at diagnosis, mean ± SD (range) | 36.1 years ± 13.4 (11–79 years) (n = 51) |
RCC metastases | |
Yes | 101/189 (53.5%) |
No | 49/189 (25.9%) |
NA | 39/189 (20.6%) |
RCC treatment | |
Nephrectomy (unspecified type) | 31/189 (16.4%) |
Nephrectomy (radical) | 25/189 (13.2%) |
Nephrectomy (partial) | 6/189 (3.2%) |
NA | 127/189 (67.2%) |