Table 1 The demographics characteristics of SMA patients (n = 101)
Variable | N (%) |
|---|---|
Child sex | Â |
 Male | 49 (48.50) |
 Female | 52 (51.50) |
Child primary diagnosis | Â |
 SMA type I | 26 (25.70) |
SMA type II | 56 (55.40) |
 SMA type III | 19 (18.80) |
Average age of SMA type (years) | Age range of SMA type (years) |
 SMA type I: 5.28 | 0.50–16.17 |
 SMA type II: 6.90 | 0.92–16.00 |
 SMA type III: 9.35 | 2.08–13.67 |
Disease duration | Age range of disease duration (years) |
 SMA type I | 4.86 (0.33–15.58) |
 SMA type II | 6.12 (0.17–15.50) |
 SMA type III | 5.9 (1.00–13.67) |
Mobility | Â |
 Non-sitter | 46 (45.50) |
 Sitter | 39 (38.60) |
 Walker | 16 (15.80) |
Stable course of disease | Â |
 No | 41 (40.60) |
 Yes | 60 (59.40) |
Skeletal deformity | Â |
 No | 27 (26.70) |
 Yes | 74 (73.30) |
Digestive system dysfunction | Â |
 No | 78 (77.20) |
 Yes | 23 (22.80) |
Medical services | Â |
 N-MS | 67 (66.30) |
 MS but not U-MDT | 21 (20.80) |
 U-MDT | 13 (12.90) |
Exercise training | Â |
 No | 56 (55.40) |
 Yes | 45 (44.60) |
Respiratory support | Â |
 No | 75 (74.30) |
 Yes | 26 (25.70) |
Nutritional support | Â |
 No | 82 (81.20) |
 Yes | 19 (18.80) |
Scoliosis surgery | Â |
 No | 99 (98.00) |
 Yes | 2 (2.00) |
Nusinersen treatment | Â |
 No | 92 (91.10) |
 Yes | 9 (8.90) |