Area (year of publication) | Prevalence (per 100,000) | Mortality | Case number |
---|---|---|---|
Northern Ireland (2006) [21] | 1: 24,956 (4.00) in 2004 | N/A | 73 patients |
Taiwan (2009) [22] | 1: 95,136 (1.05) in 2006 | N/A | 208 patients |
Quebec, Canada (2015) [23] | 1: 7872 (12.7) in 2011 | N/A | 1004 patients |
Taiwan (2016) [24] | 1: 2,500,000 (0.04) in 1997 & 1: 63,291 (1.58) in 2010 | N/A | 471 patients |
Sweden (2017) [25] | 1:18,577 (5.38) in 2013 | N/A | 551 patients |
Bath TSC Clinic, UK (2017) [12] | N/A | median age of death was 33 years (IQR 26–46) | 284 patients |