Total patients | 103 |
Male (%) | 66 (64%) |
Age (years), mean (± SD) | 60.3 (±13.1) |
Axonal sensory-motor polyneuropathy (%) | 48 (46.6%) |
Axonal sensory polyneuropathy (%) | 45 (43.7%) |
Demyelinating neuropathy (%) | 10 (9.7%) |
Sensory symptoms (%) | 85 (82.5%) |
Motor symptoms (%) | 51 (49.5%) |
Small fiber neuropathy (%) | 5 (4.8%) |
α-GAL A activity in males (mean (± SD) | 26.4 nmol/L/h (± 12.6) |
Patients with systemic symptoms or signs of FD (%) | 9 (8.7%) |