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Table 1 Baseline ECG Abnormalities Observed in the NHS Subjects. Frequency of general ECG readings (Normal/Abnormal/Borderline) and ECG abnormalities observed. Borderline ECGs grouped together with abnormal ECGs

From: Patients with ACVR1R206H mutations have an increased prevalence of cardiac conduction abnormalities on electrocardiogram in a natural history study of Fibrodysplasia Ossificans Progressiva

  Number % (N= 106)
Normal 44 41.5%
Abnormal 58 54.7%
Borderline 4 3.8%
  Number % of all Abnormal ECGs (N= 62) % of All ECGs (N= 106)
Conduction Abnormality 48   45.3%
 Nonspecific Intraventricular Conduction Delay 40 64.5% 37.7%
 Right Axis Deviation 10 16.1% 9.4%
 Nonspecific ST and T Wave Abnormality 7 11.3% 6.6%
 Right Bundle Branch Block 5 8.1% 4.7%
 Sinus Arrhythmia 5 8.1% 4.7%
 Incomplete Right Bundle Branch Block 2 3.2% 1.9%
 Left Axis Deviation 2 3.2% 1.9%
 Early Repolarization 2 3.2% 1.9%
 Long QT Interval 1 1.6% 0.9%
 Left Ventricular Hypertrophy 1 1.6% 0.9%
 Left Ventricular Hypertrophy with Repolarization Abnormality 1 1.6% 0.9%
 Ventricular Premature Complex 1 1.6% 0.9%
 First Degree AV Block 1 1.6% 0.9%