Emergency | Symptoms | EB subtype | Key references |
---|---|---|---|
Sepsis | Fever, increased CRP, leukocytosis, positive blood cultures | Any severe EB subtype | |
Acute feeding inability in newborns/infants | Feeding refusal, sialorrhea, blisters in the oral cavity | DEB | |
Acute airway obstruction | Shortness of breath, stridor, distress, dusky skin coloration | JEB | |
Acute esophageal obstruction | Painful dysphagia, aphagia, sialorrhea, regurgitation | RDEB | |
Acute urinary retention | Inability to pass urine, lower abdominal distension and pain | JEB, DEB, KEB | |
Corneal erosion | Pain, photophobia, blepharospasm, tearing | JEB, DEB, KEB |