Table 1 Characteristics of the centers and main characteristics of the patients discussed at the genetic multidisciplinary discussion (geneMDD)
From: Pilot experience of multidisciplinary team discussion dedicated to inherited pulmonary fibrosis
Number of participating centers | 34 |
|---|---|
Number of countries | 7 |
Number of patients discussed | 95 |
Number of families | 83 |
Patient age (years) (median [range]) | 43 [0–77] |
Male | 53 (56%) |
CT pattern (N = 85) | |
 UIP or probable UIP | 22 (26%) |
 Indeterminate for UIP | 32 (37%) |
 Alternative to UIP | 23 (27%) |
 No ILD | 8 (9%) |
Histology (N = 21) | |
 UIP or probable UIP | 8 (38%) |
 Alternative diagnosis | 9 (43%) |
 Unclassifiable | 4 (19%) |
Pulmonary function tests (median [range]) | |
 FVC (% of predicted value) | 68 [24–135] |
 DLCO (% of predicted value) | 52 [13–108] |