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Table 1 Subject Characteristics

From: Oral health-related quality of life in Loeys-Dietz syndrome, a rare connective tissue disorder: an observational cohort study

Variables

LDS

UFM

Total subjects (n)

33

16

Gender

 Male, % (n)

48.5 (16)

18.75 (3)

 Female, % (n)

51.5 (17)

81.25 (13)

Age

 Mean (Years)

19.6#

41.4

 SD

15.1

6.11

 Range

3–57

33–54

  1. Statistical analyses: A paired sample t-test. #Significant compared to controls (p < 0.001)
  2. LDS Loeys-Dietz Syndrome
  3. UFM Unaffected Family Member