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Table 1 Distribution of features according to the diagnostic criteria proposed by Kienast et al. [3]

From: Cutis marmorata telangiectatica congenita: a literature review

 Patients positive for these features, n (%)Patients negative for these features, n (%)Information not available (N/A), n (%)
Major criteria
 • Congenital reticulate (marmorated) erythema485 (100%)0 (0%)0 (0%)
 • Absence of venectasia4 (0.8%)99 (20.4%)382 (78.8%)
 • Unresponsiveness to local heating117 (24.1%)0 (0%)368 (75.9%)
Minor criteria
 •Fading of the erythemaa143 (29.5%)22 (4.5%)320 (66.0%)
 •Telangiectasia81 (16.7%)8 (1.6%)396 (81.6%)
 •Port-wine stain47 (9.7%)10 (2.1%)428 (88.2%)
 •Ulcerations47 (9.7%)28 (5.8%)410 (84.5%)
 •Cutaneous atrophy73 (15.1%002921 (4.3%)391 (80.6%)
  1. aOverall fading of the erythema, not just over a limited time period