Table 1 Distribution of features according to the diagnostic criteria proposed by Kienast et al. [3]
From: Cutis marmorata telangiectatica congenita: a literature review
Patients positive for these features, n (%) | Patients negative for these features, n (%) | Information not available (N/A), n (%) | |
|---|---|---|---|
Major criteria | |||
• Congenital reticulate (marmorated) erythema | 485 (100%) | 0 (0%) | 0 (0%) |
• Absence of venectasia | 4 (0.8%) | 99 (20.4%) | 382 (78.8%) |
• Unresponsiveness to local heating | 117 (24.1%) | 0 (0%) | 368 (75.9%) |
Minor criteria | |||
•Fading of the erythemaa | 143 (29.5%) | 22 (4.5%) | 320 (66.0%) |
•Telangiectasia | 81 (16.7%) | 8 (1.6%) | 396 (81.6%) |
•Port-wine stain | 47 (9.7%) | 10 (2.1%) | 428 (88.2%) |
•Ulcerations | 47 (9.7%) | 28 (5.8%) | 410 (84.5%) |
•Cutaneous atrophy | 73 (15.1%0029 | 21 (4.3%) | 391 (80.6%) |