Table 1 Clinical and laboratory characteristic of adults and children with LABD

Male patients

13 (48.1)

8 (72.7)

0.28

Mean age at diagnosis (years)

60.6

5.4

–

“String of pearls” pattern

3 (11.1)

5 (45.5)

0.03^*

Mucosal involvement

4 (14.8)

5 (45.5)

0.09

Head involvement (excluded mucosae)

6 (22.2)

8 (72.7)

0.008^*

Perioral involvement

1 (3.7)

6 (54.5)

0.001^*

Scalp involvement

4 (14.8)

0

0.3

Limbs

20 (74.1)

8 (72.7)

0.93

Trunk

15 (55.6)

6 (54.5)

1

Buttocks

4 (14.8)

1 (9.1)

1

Drug-induction

1 (3.7)

1 (9.1)

0.5

Eosinophils on histopathology

17 (62.7)

5 (45.5)

0.47

Linear IgA along the BMZ at DIF

21 (77.8)

9 (81.8)

1

Linear/granular IgA along the BMZ at DIF

6 (22.2)

2 (9.1)

1

C3c deposits at DIF

7 (25.9)

4 (36.4)

0.7

Salt-split skin IIF positivity for linear IgA^a

13 (43.5)

6 (85.7)

0.21

CR^b

21 (84)

10 (90.9)

1

PR^b

2 (8)

1 (9.1)

1

NR^b

2 (8)

0

1

Relapses^b

4 (16)

1 (9.1)

1