Skip to main content

Table 12 Guidance statements for tonsillectomy and/or adenoidectomy, tracheostomy and insertion of ventilation tubes

From: Recommendations for the management of MPS IVA: systematic evidence- and consensus-based guidance

Statement Percentage consensus
Tonsillectomy and/or adenoidectomy is recommended for patients with MPS IVA who display recurrent otitis media, snoring and/or OSA as early as possible following diagnosis without waiting for disease progression
Evidence Grade: C (level 2, 3 and 4 studies)
94%
Insertion of ventilation tubes is recommended for patients with MPS IVA with otitis media with effusion and/or recurrent otitis media to maintain hearing and/or prevent recurrent acute otitis media
Evidence Grade: D (limited published evidence)
100%
Tracheostomy is recommended in patients with MPS IVA who do not respond to any of the treatment modalities mentioned above
Evidence Grade: D (limited published evidence)
77%