From: Recommendations for the management of MPS IVA: systematic evidence- and consensus-based guidance
Statement | Percentage consensus |
---|---|
Tonsillectomy and/or adenoidectomy is recommended for patients with MPS IVA who display recurrent otitis media, snoring and/or OSA as early as possible following diagnosis without waiting for disease progression Evidence Grade: C (level 2, 3 and 4 studies) | 94% |
Insertion of ventilation tubes is recommended for patients with MPS IVA with otitis media with effusion and/or recurrent otitis media to maintain hearing and/or prevent recurrent acute otitis media Evidence Grade: D (limited published evidence) | 100% |
Tracheostomy is recommended in patients with MPS IVA who do not respond to any of the treatment modalities mentioned above Evidence Grade: D (limited published evidence) | 77% |