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Table 1 Clinical areas of focus and recommended speciality focus

From: Recommendations for the management of MPS IVA: systematic evidence- and consensus-based guidance

Table Recommended speciality focus
Table 2: General principles for the management of patients with MPS IVA all
Table 3: Recommended routine monitoring and assessments in patients with MPS IVA all
Table 4: Guidance statement for elosulfase alfa geneticist, metabolic physician, paediatrician, nurse, physiotherapist
Table 5: Guidance statement for HSCT anaesthetist, bone marrow transplant expert/hematopoietic stem cell transplant expert, geneticist, paediatrician, nurse
Table 6: Guidance statements for CPAP, NIPPV, oxygen supplementation and hypercapnia monitoring anaesthetist, ear-nose-throat specialist, geneticist, paediatrician, respiratory physician/pulmonologist, nurse
Table 7: Guidance statements for anaesthesia all
Table 8: Guidance statements for hip reconstruction, hip replacement and growth modulation surgeries anaesthetist, geneticist, orthopaedic surgeon, neurosurgeon, paediatrician, physiotherapist
Table 9: Guidance statements for decompression of the spinal cord, spinal stabilisation and thoracolumbar kyphoscoliosis anaesthetist, geneticist, orthopaedic surgeon, neurosurgeon, paediatrician, physiotherapist
Table 10: Guidance statement for corneal transplantation anaesthetist, geneticist, ophthalmologist, paediatrician
Table 11: Guidance statement for cardiac valve replacement anaesthetist, cardiologist, geneticist, paediatrician
Table 12: Guidance statements for tonsillectomy and/or adenoidectomy, tracheostomy and insertion of ventilation tubes anaesthetist, geneticist, ear-nose-throat specialist, paediatrician, respiratory physician/pulmonologist