Table 2 Demographic/clinical characteristics and duration of follow-up of patients with ≥1 year of follow-up
Characteristic | Value |
|---|---|
Total cases, n (%) | 265 (100.0) |
Male, n (%) | 118 (44.5) |
Median (IQR) age at anchor visit, yearsa | 4.0 (0.4–34.0) |
Reported family history of HPP, n (%) | 74 (27.9) |
Age at first reported occurrence of HPP manifestations, n (%) | |
In utero | 30 (11.5) |
Infancy/early childhood (< 2 years) | 101 (38.7) |
Childhood (2 to < 10 years) | 78 (29.9) |
Adolescence (10 to < 18 years) | 9 (3.4) |
Adulthood (≥ 18 years) | 43 (16.5) |
Median (IQR) duration of follow-up by age at first reported occurrence of HPP manifestations, years | |
Overall | 7.0 (3.0–18.0) |
In utero | 4.0 (2.1–10.3) |
Infancy/early childhood (< 2 years) | 5.4 (2.4–14.8) |
Childhood (2 to < 10 years) | 7.7 (3.6–28.5) |
Adolescence (10 to < 18 years) | 6.0 (4.3–27.0) |
Adulthood (≥ 18 years) | 15.0 (6.3–27.0) |