Table 4 Comparison of height, weight, 6MWT, post- 6MWT fatigue minus Pre-6MWT fatigue for identical subjects with BTHS (n = 18) between 2014 and 2016. Fatigue assessed using the Modified Borg Scale
From: Functional exercise capacity, strength, balance and motion reaction time in Barth syndrome
ID | Age 2014 (years) | Age 2016 (years) | Height 2014 cm (Z-Score)a | Height 2016 cm (Z-Score)a | Weight 2014 kg (Z-Score)a | Weight 2016 kg (Z-Score)a | 6 MWT 2014 (m) | 6 MWT 2016 (m) | Change (m) | Post-Pre Fatigue 2014 | Post-Pre Fatigue 2016 |
|---|---|---|---|---|---|---|---|---|---|---|---|
1 | 6 | 8 | 112.4 (−1.33) | 128 (−0.8) | 20 (− 0.91) | 27 (− 0.26) | 313.9 | 276 | −37.9 | 0 | 1 |
2 | 9 | 11 | 122.5 (−1.86) | 135 (− 1.26) | 19 (−3.54) | 23 (−3.06) | 436.8 | 360 | −76.8 | 0.5 | 3 |
3 | 9 | 11 | 136 (−0.182) | 147 (− 0.04) | 24 (−1.7) | 31 (− 1.32) | 405.4 | 455 | 49.6 | 0.5 | 0 |
4 | 9 | 12 | 121.3 (−2.69) | 128 (−3.6) | 21 (− 2.99) | 25 (−3.77) | 411.5 | 325.7 | −85.8 | 1 | 1 |
5 | 10 | 12 | 133 (−1.0) | 142 (−1.06) | 24 (−2.07) | 28 (− 2.29) | 457.2 | 405 | −52.2 | 3 | 2.5 |
6 | 10 | 12 | 139.5 (−0.43) | 149 (−0.71) | 35 (− 0.08) | 41 (− 0.43) | 404.2 | 453 | 48.8 | 4 | 3.5 |
7 | 13 | 15 | 134.3 (−3.40) | 140 (−2.74) | 25 (− 4.62) | 31 (− 3.00) | 332.8 | 355.2 | 22.4 | −2 | −3 |
8 | 14 | 16 | 155 (−1.57) | 173 (−0.26) | 35 (−2.82) | 42 (−2.96) | 363.3 | 461 | 97.7 | −0.5 | 0.5 |
9 | 16 | 18 | 163.6 (−1.38) | 173 (−0.47) | 37 (−3.68) | 40 (−4.24) | 345.3 | 376.1 | 30.8 | 2 | 3 |
10 | 17 | 19 | 172.8 (−0.41) | 178 (0.18) | 41 (−3.66) | 47(− 3.02) | 358.1 | 300.6 | −57.5 | 0 | 0 |
11 | 19 | 21 | 175.5 (−0.16) | 177 | 58 (−1.19) | 62 | 536.4 | 560.2 | 23.8 | 0 | 2 |
12 | 20 | 23 | 168.8 | 168 | 52 | 59 | 403.6 | 392 | −11.6 | 3.5 | 1 |
13 | 21 | 23 | 165.8 | 169 | 65 | 74 | 405.4 | 398.2 | −7.2 | 2 | 3 |
14 | 21 | 24 | 180.8 | 183 | 66 | 76 | 315.5 | 386 | 70.5 | 1.5 | 7 |
15 | 24 | 26 | 165 | 165 | 44 | 45 | 407.8 | 354 | −53.8 | 0 | 0 |
16 | 25 | 27 | 179.3 | 179 | 63 | 57 | 349 | 486 | 137 | 3 | 3 |
17 | 32 | 34 | 186.2 | 186 | 89 | 83 | 278 | 336 | 58 | 0 | 1 |
18 | 32 | 34 | 168.5 | 169 | 64 | 68 | 301.8 | 300 | −1.8 | 0 | 0 |