Table 2 Patient characteristics
Characteristics | Data completeness, n (%) | Â |
|---|---|---|
Sex, n (%) | 2700 (100%) | Â |
 Male |  | 1294 (47.9) |
 Female |  | 1406 (52.1) |
Age at diagnosis, years, | 2700 (100%) | Â |
 Median (Min; Max) |  | 31.0 (4; 89) |
 Mean (SD) |  | 31.4 (19.6) |
N (%) | ||
 4–10 |  | 460 (17.0) |
 11–20 |  | 475 (17.6) |
 21–40 |  | 939 (34.8) |
 41–60 |  | 565 (21.0) |
  > 60 |  | 261 (9.7) |
Age at onset, years, | 2236 (82.8%) | Â |
 Median (Min; Max) |  | 18.0 (0; 81) |
 Mean (SD) |  | 22.4 (19.0) |
N (%) | ||
 ≤ 10 |  | 829 (37.1) |
 11–20 |  | 401 (17.9) |
 21–40 |  | 601 (26.9) |
 41–60 |  | 309 (13.8) |
 > 60 |  | 96 (4.3) |
Diagnostic delay, years | 2236 (82.8%) | Â |
 Median (Min; Max) |  | 4.0 (0; 69) |
 Mean (SD) |  | 8.8 (11.4) |
N (%) | ||
 0 (diagnosis in the year of symptoms onset) |  | 357 (16.0) |
 1–4 |  | 769 (34.4) |
 5–9 |  | 443 (19.8) |
 10–20 |  | 380 (17.0) |
 ≥ 21 |  | 287 (12.8) |
Period of diagnosis, n (%) | 2700 (100%) | Â |
 ≤ 1980 |  | 101 (3.7) |
 1980–1999 |  | 734 (27.2) |
 ≥ 2000 |  | 1865 (69.1) |
Consanguinity, n (%) | 1488 (55.1%) | Â |
 With consanguinity |  | 68 (4.6) |
With records on immunoglobulin replacement therapy, n (%) | 2290 (84.8%) | Â |