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Table 2 Patient characteristics

From: The burden of common variable immunodeficiency disorders: a retrospective analysis of the European Society for Immunodeficiency (ESID) registry data

Characteristics Data completeness, n (%)  
Sex, n (%) 2700 (100%)  
 Male   1294 (47.9)
 Female   1406 (52.1)
Age at diagnosis, years, 2700 (100%)  
 Median (Min; Max)   31.0 (4; 89)
 Mean (SD)   31.4 (19.6)
N (%)
 4–10   460 (17.0)
 11–20   475 (17.6)
 21–40   939 (34.8)
 41–60   565 (21.0)
  > 60   261 (9.7)
Age at onset, years, 2236 (82.8%)  
 Median (Min; Max)   18.0 (0; 81)
 Mean (SD)   22.4 (19.0)
N (%)
 ≤ 10   829 (37.1)
 11–20   401 (17.9)
 21–40   601 (26.9)
 41–60   309 (13.8)
 > 60   96 (4.3)
Diagnostic delay, years 2236 (82.8%)  
 Median (Min; Max)   4.0 (0; 69)
 Mean (SD)   8.8 (11.4)
N (%)
 0 (diagnosis in the year of symptoms onset)   357 (16.0)
 1–4   769 (34.4)
 5–9   443 (19.8)
 10–20   380 (17.0)
 ≥ 21   287 (12.8)
Period of diagnosis, n (%) 2700 (100%)  
 ≤ 1980   101 (3.7)
 1980–1999   734 (27.2)
 ≥ 2000   1865 (69.1)
Consanguinity, n (%) 1488 (55.1%)  
 With consanguinity   68 (4.6)
With records on immunoglobulin replacement therapy, n (%) 2290 (84.8%)