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Fig. 3 | Orphanet Journal of Rare Diseases

Fig. 3

From: Cholic acid for primary bile acid synthesis defects: a life-saving therapy allowing a favorable outcome in adulthood

Fig. 3

Evolution during long-term CA therapy of liver pathology in patient 15 (a and b) and patient 14(c and d) with Δ4–3-oxosteroid 5β-reductase deficiency. a Liver histology after 5.5 years of combined UDCA plus CA therapy. b Liver histology after 16 years of combined UDCA plus CA therapy. c Liver histology after 5.5 years of CA therapy. d Liver histology after 16 years of CA therapy. See Table 2 for fibrosis scores

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Orphanet Journal of Rare Diseases

ISSN: 1750-1172