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Table 3 Echocardiographic features of the 32 patients with MPS IVA and the relationships between severity of cardiac valve abnormalities and age

From: Cardiac features and effects of enzyme replacement therapy in Taiwanese patients with Mucopolysaccharidosis IVA

Echocardiographic features

MS

MR

AS

AR

TS

TR

PS

PR

MVP

Thick IVS

%

38%

22%

38%

9%

0%

6%

0%

0%

22%

31%

r value (severity of cardiac valve abnormalities versus age)

0.329

0.109

0.582

0.638

ND

0.008

ND

ND

0.062

0.530

p value

p>0.05

p>0.05

p<0.01

p<0.01

p>0.05

p>0.05

p>0.05

p>0.05

p>0.05

p<0.01

  1. MPS mucopolysaccharidosis, MS mitral stenosis, MR mitral regurgitation, AS aortic stenosis, AR aortic regurgitation, TS tricuspid stenosis, TR tricuspid regurgitation, PS pulmonary stenosis, PR pulmonary regurgitation, MVP mitral valve prolapse, IVS interventricular septum