Cardiac features and effects of enzyme replacement therapy in Taiwanese patients with Mucopolysaccharidosis IVA

Table 3 Echocardiographic features of the 32 patients with MPS IVA and the relationships between severity of cardiac valve abnormalities and age

Echocardiographic features	MS	MR	AS	AR	TS	TR	PS	PR	MVP	Thick IVS
%	38%	22%	38%	9%	0%	6%	0%	0%	22%	31%
r value (severity of cardiac valve abnormalities versus age)	0.329	0.109	0.582	0.638	ND	0.008	ND	ND	0.062	0.530
p value	p>0.05	p>0.05	p<0.01	p<0.01	p>0.05	p>0.05	p>0.05	p>0.05	p>0.05	p<0.01

MPS mucopolysaccharidosis, MS mitral stenosis, MR mitral regurgitation, AS aortic stenosis, AR aortic regurgitation, TS tricuspid stenosis, TR tricuspid regurgitation, PS pulmonary stenosis, PR pulmonary regurgitation, MVP mitral valve prolapse, IVS interventricular septum

ISSN: 1750-1172