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Table 2 The values of echocardiographic parameters and their relationships with age in the 32 patients with MPS IVA

From: Cardiac features and effects of enzyme replacement therapy in Taiwanese patients with Mucopolysaccharidosis IVA

Echocardiographic parameters LVMI (z score) RVDd (z score) IVSd (z score) IVSs (z score) LVIDd (z score) LVIDs (z score) LVPWd (z score) LVPWs (z score) AoD (z score) LAD (z score)
Mean (SD) 0.94 1.20 2.70 1.02 0.56 −0.16 0.39 −0.10 3.26 0.22
(2.24) (1.74) (3.02) (1.85) (1.52) (1.06) (1.32) (1.34) (1.64) (1.29)
r value (echocardiographic parameter versus age) 0.647 −0.276 0.458 0.544 0.248 −0.085 0.409 0.563 0.582 −0.156
p value p < 0.01 p > 0.05 p < 0.01 p < 0.05 p > 0.05 p > 0.05 p < 0.05 p < 0.01 p < 0.01 p > 0.05
  1. MPS, mucopolysaccharidosis; LVMI, left ventricular mass index; RVDd, right ventricular end diastolic dimension; IVSd, interventricular septum thickness in diastole; IVSs, interventricular septum thickness in systole; LVIDd, left ventricular internal diameter in diastole; LVIDs, left ventricular internal diameter in systole; LVPWd, left ventricular posterior wall thickness in diastole; LVPWs, left ventricular posterior wall thickness in systole; AoD, aortic diameter; LAD: left atrial dimension; SD, standard deviation