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Table 1 Classification of angioedema (adapted from Craig et al. [7])

From: Epidemiology of Bradykinin-mediated angioedema: a systematic investigation of epidemiological studies

Bradykinin-Mediated Angioedema

C1-INH Deficiency / Defect

C1-INH Normal

Inherited

Acquired

Inherited

Acquired

HAE-1 & HAE-2

C1-INH-AAE

HAE-3

ACEI-AE

  1. C1-INH-AAE acquired angioedema due to C1 inhibitor deficiency, ACEI-AE angiotensin-converting enzyme induced angioedema, HAE-1 hereditary angioedema due to C1 inhibitor deficiency, HAE-2 hereditary angioedema due to C1 inhibitor defect, HAE-3 hereditary angioedema with normal C1 inhibitor levels