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Fig. 2 | Orphanet Journal of Rare Diseases

Fig. 2

From: Fatal thoracic aortic aneurysm and dissection in a large family with a novel MYLK gene mutation: delineation of the clinical phenotype

Fig. 2

Computerized Tomography angiography- CTA of patient VI-26. CTA demonstrated Type-3B aortic dissection (Arrow, sagittal planes a (2008), b, c, (2011)) beginning distal to left subcalvian artery (LTSCA) that continued down 12 mm above to the bifurcation of iliac arteries (planes a, b, c and transverse panel e). The celiac artery, SMA and rt. renal artery emerged apparently from the true aortic space while, the left renal artery seemed atrophic and emerged from the false lumen (panel d). The inferior mesenteric artery (IMA) emerged from the false lumen (plane c). The aortic artery diameters were within the normal ranges along 8 years of follow-up. The iliac arteries looked normal and also the perfusion of the splanchnic system and lower extremities. In the last CTA study (2011), in addition to the old findings, a new finding (Panels f, g) of a dissection of the innominate artery (f) continuing into the right subclavian artery (g), with no evidence for dissection in the right carotid artery, was demonstrated

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