Patient no. | Sex | Genotype | Diagnosis age (yr) | Age at Cx onset (yr) | Duration until Cx onset (yr) | BMI, kg/m2 at Dx with DM | BMI, kg/m2 at Dx with Cx | A1C (%) at Dx with DM | A1C (%) at Dx with Cx | HOMA-IR | Duration of GHT | Duration of DM | Type of DMT | Type of Cx | |
---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
PWS | DM | ||||||||||||||
5 | M | Del | 10.1 | 15.0 | 23.5 | 8.5 | 47.55 | 38.25 | 7.3 | 14.0 | 7.7 | NA | 13.3 | M- > M + S- > R- > N + M + S- > M + S- > M | DR |
14 | M | Del | 1.8 | 13.8 | 15.0 | 1.2 | 22.53 | 25.28 | 9.6 | 7.2 | 8.5 | 3 | 2.0 | M + B- > M | DR |
75 | M | Del | 0.2 | 17.8 | 23.0 | 5.2 | 41.82 | 40.48 | 9.4 | 9.7 | 7.9 | 1.2 | 5.5 | M + S- > M + S + B | DR |
12 | F | Del | 4.8 | 14.7 | 19.0 | 4.3 | 30.48 | 29.59 | 6.9 | 11.3 | 10.2 | 7.5 | 5.0 | M- > M + S- > M + S + B- > M + B + G | DR |
44 | F | Del | 8.0 | 18.5 | 22.5 | 4.0 | 32.51 | 31.47 | 8.7 | 6.7 | 7.0 | 1.8 | 4.8 | M | DN (Mi), DPN |
55 | F | Del | 13.3 | 14.2 | 24.2 | 10.0 | 51.40 | 55.46 | 6.7 | 12.0 | 9.5 | NA | 11.4 | M > M + S- > M + S + α- > M + S + α + G- > B + R + M | DN (P) |
77 | F | Del | 27.0 | 27.0 | 27.0 | 0.0 | 40.20 | 40.20 | 12.1 | 12.1 | 7.6 | NA | 5.7 | M + S + B | DN (Mi), DR, DPN |